Abstract. Background: Hypertrophic pachymeningitis is an uncommon disorder that causes a localized or diffuse thickening of the dura mater and has been. Summary: Idiopathic hypertrophic cranial pachymeningitis is a rare inflammatory disease with diffused involvement of the dura. Often, the definite diagnosis is. Hypertrophic pachymeningitis is a unique clinical entity characterised by fibrosis and thickening of the duramater with resulting neurological dysfunction.

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A case of chronic hypertrophic cranial pachymeningitis causing cranial polyneuropathy and unilateral central retinal vein occlusion.

Presence of associated leptomeningeal enhancement or parenchymal abnormalities with the exception of brain edema should suggest an alternate diagnosis. Check for errors and try again. Idiopathic hypertrophic cranial pachymeningitis. Long term improvement of idiopathic hypertrophic cranial pachymeningitis by lymphocytapheresis.

Case records of the Massachusetts general hospital. Clin Exp Neurol ; Log in Sign up. Churchill livingstone ; New York. The main clinical features were headache and cranial nerve palsies.


Neuropathological findings of six cases including two autopsied cases are also presented. Pachymeningitis cervicalis hypertrophica syphilitica.

Four patients underwent biopsy of the dura, and the pathological study showed non-specific inflammatory changes.

One case had necrotizing vasculitis of the small arteries located in the dura and the cerebral surface. On clinical examination, she had no perception of light in both the eyes and ophthalmoscopic examination showed obliteration of cup with slightly hyperemic fundi.

Idiopathic hypertrophic pachymeningitis.

A year-old lady presented with headache and progressive painless loss of vision in both the eyes over a periods of 6 months. Rinsho Shinkeigaku ; Enhanced MR imaging of hypertrophic pachymeningitis. Online since 20 th March ‘ Combined therapy of corticosteroid and azathioprine in hypertrophic cranial pachymeningitis.

J Neurol Neurosurg Psychiatry ; Acta Derm Venereol ; Clinicoradiological spectrum and therapeutic options. Open in a separate window. Unable to process the form. Eur J Radiol ; Presse Med ; A year-old male came to ER with headache associated with vomiting since 2 weeks and 1 episode of right focal seizure.

This is an open-access article distributed under the terms of the Creative Commons Pachymeningitie Alike 3. Hypertrophic cranial pachymeningitis involving the pituitary gland: T1 contrast coronal MRI image showing diffuse enhancement with thickening of meninges. Cranial pachymeningitis typically cause progressive cranial nerve palsies, headaches, and cerebellar dysfunction.


The cell infiltration was marked at the surface of the dura mater. Published by Wolters Kluwer – Medknow. N Engl J Padhymeningitis Idiopathic hypertrophic cranial pachymeningitis: Hypertrophic pachymeningitis can be diagnosed with contrast MRI of brain when the clinician maintains a high index of suspicion for this condition.

Idiopathic hypertrophic pachymeningitis.

Rest of the neurological examination was normal. Multiple meningiomas Multiple meningiomas.

Coronal MR imaging showing diffuse dural enhancement and thickening, along with left parieto occipital edema. Axial section of MRI image showing diffuse enhacement with thickening of meninges.

An unusual cause of subacute and chronic headache.